Werdnig-Hoffman disease
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Werdnig-Hoffman disease Definition
(n)
autosomal
recessive
disease
in
which
the
degeneration
of
spinal
nerve
cells
and
brain
nerve
cells
leads
to
atrophy
of
skeletal
muscles
and
flaccid
paralysis
;
death
usually
occurs
in
early
childhood
Werdnig-Hoffman disease Synonyms
Werdnig-Hoffman disease
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